Lichen Planus
Lichen Dermatoses
Quiz
Resources
Keratosis lichenoides chronica (also known as Nekam’s disease)
- Unknown
- Unknown
- Violaceous, keratotic, lichenoid papules in a symmetrical, linear and reticulated pattern on limbs and trunk
- Greasy and scaly lesions or psoriasiform scaly plaques on the upper face + keratotic papules on palms and soles
- ± nail and scalp involvement
- Chronic and progressive course, but some lesions can regress (summer and aging)
- Similar histologic and immunofluorescence findings as lichen planus
- Unknown
Symptomatic treatment (usually unsatisfactory):
- Topical corticosteroids
- Systemic corticosteroids
- Methotrexate, cyclosporine A
- Etretinate
- Oral vitamin A
- Psoralen and ultraviolet A/Narrowband ultraviolet B